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Intermediate filament Alternative splicing ARN Humans Astrocytes Transcriptomics Exercise ACETYLCHOLINESTERASE Male Dilated cardiomyopathy Mouse models Maximal force Mice Brain Myotonic Dystrophy Type 1 GSK3␤ Antisense oligonucleotides CONGENITAL MYATHENIC SYNDROME Glial cells Cell culture model Oligodendrocyte Hypoxia Antisense oligonucleotide Glutamate DMSXL mice GABA Acetylcholinesterase knockout mouse Brain dysfunction Cytoskeleton KNOCKOUT MICE Myotonic dystrophy PCR RNA biology Transgenic mouse RNA splicing Cell model CMS Astrocyte Aging MBNL Animals Myotonic dystrophy type 1 DMPK AAV Myotonic Dystrophy CTG repeat instability Neuron Long read sequencing Quantitative microdialysis CRISPR/Cas9 PacBio Autophagy Glucocorticoids Gene therapy Heart failure Muscular dystrophy Central nervous system CTG repeat contractions Transgenic mouse model Muscle Dystrophin Therapy Trinucleotide repeat expansion Knockout Myotonic dystrophy mouse models Cell penetrating peptide Oligodendrocytes Gene editing Myostatin Fibrosis Motoneuron DM1 Acetylcholinesterase deficiency Gene Therapy Duchenne muscular dystrophy Exercice Skeletal muscle Myelin Genotype phenotype correlation CTG repeats Thérapie génique Acute coronary syndrome In vivo BIOLOGIE MOLECULAIRE Dystrophie Myotonique Mouse model Heart Dynamin 2 Glucocorticoid-receptor Desmin Centronuclear myopathy Trinucleotide Repeat Expansion Myotonic Dystrophy type 1 RNA interference Diaphragm Dystrophie myotonique CRISPRi Lc3 Expression Cardiac muscle